For which condition would an infant born with exstrophy of the bladder be at risk?

Epidemiology of bladder exstrophy and epispadias: a communication from the International Clearinghouse for Birth Defects Monitoring Systems

No authors listed. Teratology. 1987 Oct.

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  • Epidemiology of bladder exstrophy and epispadias: a communication from the International Clearinghouse for Birth Defects Monitoring Systems
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  • Which concern would be a priority for the nurse caring for an infant born with exstrophy of the bladder?
  • Which covering would the nurse use over the exposed area of an infant admitted with exstrophy of the bladder?
  • Which concern is most commonly expressed by NICU parents?
  • Which assessment findings would the nurse recognize as common in infants with Down syndrome?

Abstract

A study of infants with bladder exstrophy or epispadias was based on data from ten malformation monitoring systems around the world. The material is derived from nearly 6.3 million births. The recorded prevalence at birth of bladder exstrophy was 3.3 per 100,000 births and of epispadias (without bladder exstrophy) 2.4 per 100,000. The recorded rates of bladder exstrophy did not vary between the monitoring systems, but the rates of epispadias did. Furthermore, nearly all registered infants with epispadias were males. The sex ratio for bladder exstrophy was 1.5:1. Perinatal deaths occurred mainly when other malformations were also present. There was an increased risk in this group of malformations in infants of women aged less than 20 years. At high parity (3+), an increased risk was observed for bladder exstrophy, but there was a decreased risk for epispadias. The birth weight distribution was shifted slightly more to the left in isolated bladder exstrophy than in isolated epispadias, but was considerably shifted to the left when other malformations existed with bladder exstrophy. Most infants with other malformations belonged to the cloacal exstrophy sequence. There was no definite time trend between 1970 and 1985 in the prevalence at birth of bladder exstrophy. The study demonstrates how data from different monitoring registries can be pooled to characterize a rare malformation.

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Which concern would be a priority for the nurse caring for an infant born with exstrophy of the bladder?

The primary goal when caring for a child with bladder exstrophy is to: preserve normal kidney function. develop adequate bladder function and promote urinary continence.

Which covering would the nurse use over the exposed area of an infant admitted with exstrophy of the bladder?

After delivery, the bladder is covered with a clear plastic dressing to protect it. Children born with bladder exstrophy are treated with reconstructive surgery after birth.

Which concern is most commonly expressed by NICU parents?

Most parents express feelings of guilt after the birth of a sick or premature baby.

Which assessment findings would the nurse recognize as common in infants with Down syndrome?

On physical examination, patients with trisomy 21 have characteristic craniofacial findings, such as the following: Physical characteristics: a small chin, slanted eyes, poor muscle tone, a flat nasal bridge, and a single crease of the palm. Flat occiput and a flattened facial appearance.

What abnormalities are associated with bladder exstrophy?

In classic bladder exstrophy, most anomalies are related to defects of the abdominal wall, bladder, genitalia, pelvic bones, rectum and anus. Bladder exstrophy is a rare developmental abnormality that is present at birth (congenital) in which the bladder and related structures are turned inside out.

Which clinical manifestations are common in infants with exstrophy of the bladder?

Signs that your baby may have bladder exstrophy include:.
A bladder that doesn't empty as expected..
Separated pubic bones (bones that form the pelvis)..
Smaller-than-usual genitalia..
An umbilical cord that connects lower on the belly than usual..

Which is a care priority for a newborn diagnosed with bladder exstrophy?

Babies born with this condition generally receive at least one bladder exstrophy surgery, but most children require multiple operations. The first priority is to close the bladder, the back of the urethra and the pelvic bones, while ensuring that the internal organs are enclosed within the abdomen.

Does bladder exstrophy cause infertility?

Most of the male and female patients with EEC have adequate sexual function. Most of the female patients have normal fertility while most of the male patients have significantly low fertility.